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Archive

Winter 2018, Vol. 26 No. 4

Hong Kong J. Dermatol. Venereol. (2018) 26, 185-188


Case Report

Dermatofibrosarcoma Protuberans presenting as an atrophic patch. A case report and brief review of literature

一宗呈現為萎縮性斑的隆突性皮膚纖維肉瘤病例報告和簡要文獻回顧

R Rafiei, K Gharaei Nejad, H Eftekhari, A Darjani, N Alizadeh

Abstract
Background: Dermatofibrosarcoma Protuberans is a fibroblastic skin tumour which tends to have locally aggressive behaviour. It usually presents as a slow-growing red-blue nodule. Presentation as an atrophic patch in adults is quite uncommon. Case Presentation: A 30-year-old female presented with a 5-month history of an atrophic patch on the right shoulder. Dermatofibrosarcoma Protuberans was confirmed with routine and immunohistochemical staining. The patient was treated with wide local excision. Conclusion: Although Dermatofibrosarcoma Protuberans is an indolent slow-growing tumor, considering its local subclinical deep extension, initial wide local excision with safe margin is highly recommended.

背景:隆突性皮膚纖維肉瘤是一種成纖維細胞皮膚腫瘤,傾向有局部侵襲性的表現。它通常表現為生長緩慢的紅藍色結節,在成人中表現為萎縮性斑塊實屬罕見。病例報告:一名30歲的女性患者,其右肩有著為時五個月的萎縮性斑塊,通過常規和免疫組織化學染色確診為隆突性皮膚纖維肉瘤,患者其後接受了廣泛性局部切除手術。結論:儘管隆突性皮膚纖維肉瘤是一種低惡性緩慢生長的腫瘤,考慮到其局部亞臨床深度延伸,故強烈建議進行包含安全邊緣的初始廣泛性局部切除。

Keywords: Dermatofibrosarcoma Protuberans, sarcoma, skin neoplasm

關鍵詞: 隆突性皮膚纖維肉瘤、肉瘤、皮膚腫瘤