Table of Content

Archive

Spring 2001, Vol. 9 No. 1

H.K. Dermatol. Venereol. Bull. (2001) 9, 10-16


Review Article

Pityriasis Rubra Pilaris: an Update Review

YP Fung

Abstract
Patients with pityriasis rubra pilaris (PRP) can sometimes be difficult to distinguish from those with psoriasis. The lack of pathognomonic markers and specific clinical and histological diagnostic criteria has made studies of PRP difficult to conduct and interpret. At least three different classification systems had been proposed to categorize patients. Those with atypical forms of PRP may represent variants of other ichthyotic disorders. The aetiology of PRP remains unknown. The role of focal acantholytic dyskeratosis as a distinguishing histological feature remains controversial. Systemic retinoid is currently the first line treatment for those with severe disease.